Medicina (Kaunas) 2010; 46 (3): 193-199
Heart transplantation in an adult patient with isolated noncompaction of the left ventricular myocardium
Sigita Glaveckaitė1, Kęstutis Ručinskas1, Jelena Čelutkienė1, Vytė Maneikienė1, Diana Zakarkaitė1, Sigita Aidietienė1, Nomeda Valevičienė2, Mindaugas Matačiūnas2, Edvardas Žurauskas3, Pranas Šerpytis1, Aleksandras Laucevičius1
1Clinic of Heart and Vascular Medicine, Faculty of Medicine, Vilnius University, 2Clinic of Chest Diseases, Allergology and Radiology, Faculty of Medicine, Vilnius University, 3Center of Pathology, Faculty of Medicine, Vilnius University, Lithuania
Key words: isolated noncompaction of the left ventricular myocardium; echocardiography; computed tomography; cardiovascular magnetic resonance; heart transplantation.
Summary. Isolated noncompaction of the ventricular myocardium is defined as a rare cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibers and meshwork, an important process in myocardial development, in absence of any coexisting congenital heart lesions. A lot of controversies exist about diagnostic criteria, nomenclature, origin, pathogenesis, and prognosis of this disease. Here, we describe an adult patient with isolated left ventricular noncompaction who presented with worsening congestive heart failure and was successfully treated with heart transplantation.
Correspondence to S. Glaveckaitė, Clinic of Heart and Vascular Medicine, Faculty of Medicine, Vilnius University, Santariškių 2, 08661 Vilnius, Lithuania. E-mail: email@example.com
Received 26 January 2009, accepted 5 March 2010